Abstract
Ehlers-Danlos syndrome (EDS) is a rare connective tissue disorder, usually characterized
by the triad of hypermobility of the joints, hyperextensibility of the skin, and tissue
fragility. Numerous gastrointestinal complications have been reported with this syndrome.
However, spontaneous diaphragmatic rupture remains a very rare complication. We report
a case of a 22-year-old woman with EDS who presented to the Emergency Department complaining
of shortness of breath and left-sided chest pain. She was ultimately found to have
a spontaneous diaphragmatic rupture after forceful emesis.
Keywords
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References
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Article info
Publication history
Published online: April 25, 2008
Accepted:
August 8,
2007
Received in revised form:
April 25,
2007
Received:
September 26,
2005
Identification
Copyright
© 2011 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
