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Hemophilia and von Willebrand Disease: A Review of Emergency Department Management

      Abstract

      Background

      Hemophilia and von Willebrand disease (VWD) are the most common congenital coagulation factor deficiencies. Patients with these disorders who experience bleeding complications are often initially managed in the emergency department (ED).

      Objective of the Review

      This review will focus on the emergency department management of patients with these disorders and provide an update on current treatment options.

      Discussion

      The mainstay of management is initial stabilization, control of bleeding when possible, and administration of specific factors. Early coordination of care with hematology is critical.

      Conclusions

      Emergency medicine providers must have an understanding of the pathophysiology, clinical presentation, and management strategies in order to optimally care for these complex patients.

      Keywords

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      Linked Article

      • Emergency Management of Hemophilia
        Journal of Emergency MedicineVol. 59Issue 4
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          We read with interest the review article by Tebo et al., which we hope will help raise awareness of hemophilia and von Willebrand disease among emergency physicians (1). We would like to emphasize and clarify some aspects of the urgent assessment and management of such patients in the emergency department.
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